Objective:To discuss the diagnosis and treatment of sinonasal malignant melanoma so as to improve the diagnosis and treatment level of the disease. Methods:Clinical data of 17 cases with sinonasal malignant melanoma treated in our department from March 1980 to June 2011 was retrospectively analyzed. Including the clinicopathological features, diagnosis, optimal treatment, and prognosis. Results:The main symptoms of sinonasal malignant melanoma were unilateral nasal obstruction, bloody nasal discharge and headache. The tumor originated mainly from the lateral wall of the nasal cavity and nasal septum. Died due to local recurrence and systemic metastasis. In the 14 cases with surgical treatment, the 3-and 5-year survival rates were 36.4% and 22.2% respectively. Conclusions:Sinonasal malignant melanoma is highly malignant with poor prognosis due to local recurrence and systemic metastasis. Early diagnosis and complete surgical resection combined with postoperative radiotherapy, chemotherapy and/or immunotherapy are essential to improve the survival rate.