Otosclerosis is a disease that manifests as a complete conductive or mixed hearing loss with intact tympanic membrane. The diagnosis of otosclerosis mainly relies on a detailed medical history and accurate audiological examination, and imaging plays a supporting role. In recent years, with the development of technology, imaging has become more and more important in the diagnosis and treatment of otosclerosis, such as preoperative diagnosis, differential diagnosis, preoperative evaluation of surgical difficulty, prediction of complications, postoperative analysis of complications, and evaluation of surgical effect and so on. This article reviews the research progress of otosclerosis imaging by consulting related literature.